English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.
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If you are a member of the AEDV: Health care resources for this disease Expert centres 69 Diagnostic tests 0 Patient organisations 21 Orphan drug s 0.
Systemic manifestations are progressive and may lead to serious complications: Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has been tested successfully in one case with intestinal and CNS manifestations. In early stages, histology of lesions may reveal a superficial and deep perivascular lymphocytic infiltration with distinct mucin nefermedad. SRJ is a prestige metric based on the idea that not all citations are the same. Other search option s Alphabetical list.
Disease definition Malignant atrophic papulosis MAP is a rare, envermedad, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white degps and a surrounding teleangiectatic rim. This condition is chronic and lesions persist over years, often throughout life.
Pemphigus Vegetans in the Inguinal Folds.
All articles are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style. Differential diagnosis The histology of early lesions resembles cutaneous lupus enfermedax see this term. Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial cells have been proposed.
As all patients may potentially develop the systemic, life-threatening variant, an annual follow-up is mandatory. Subscribe to our Newsletter.
enfermedad de Degos – English Translation – Word Magic Spanish-English Dictionary
Specialised Social Services Enfernedad directory. Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Summary Epidemiology Less than cases have been described in the literature. Face, scalp, palms of hands and soles of feet are rarely involved. Degoa description MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities.
You can change the settings or obtain more information by clicking here. Many patients have been reported to have defects in blood coagulation. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted.
Diagnosis is based primarily on the cutaneous clinical picture that enfermdad nearly pathognomonic.
Previous article Next article. Genetic counseling A genetic predisposition with an autosomal dominant trait has been suggested. Show more Show less. More developed lesions show prominent changes in the dermoepidermal junction, with atrophy of the epidermis and an area of sclerosis in the papillary dermis. Are you a health enfermedaf able to prescribe or dispense drugs?
Subscriber If you already have your login data, please click here. SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field. Ocular involvement, which affects the eyelids, conjuctiva, retina, sclera and the choroid plexus, as well as the development of diplopia and ophthalmoplegia as secondary side effects of the neurologic involvementhas also been described.
Summary and related texts. For all other comments, please send your remarks via contact us. Systemic lesions may affect the gastrointestinal tract and the central nervous system CNS and are potentially lethal. It may more rarely manifest as pericarditis or in other organs such as the lungs, presenting as pleuritis.
Later a wedge-shaped connective ddegos necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs. A clinical inspection of the skin should be combined with additional examinations including brain magnetic resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and abdominal ultrasound, in order to assess the long-term prognosis.
Term Bank – enfermedad de degos – Spanish English Dictionary
More developed lesions can imitate lichen sclerosus see this term. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for enfeemedad or treatment.
Read this article in English. Diagnostic methods Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic.
Etiology The etiopathogenesis of the disease remains unknown. MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities.
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Check this box if you wish to receive a copy of your message. From Monday to Friday from 9 a. Additional information Further information on this disease Classification s 3 Gene s 0 Clinical signs and symptoms Publications in PubMed Other website s 7.
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